Clinical UM Guideline

 

Subject: Surgical Strabismus Correction
Guideline #:  CG-SURG-41 Publish Date:    03/29/2018
Status: Reviewed Last Review Date:    02/27/2018

Description

This document addresses strabismus, which refers to eyes that are not properly aligned.  Examples of strabismus include one or both eyes that are intermittently or constantly turned in towards the nose (esotropia) or out (exotropia).  Strabismus surgery involves surgical weakening or strengthening of the ocular muscles to correct the ocular alignment.  The goals of strabismus surgery are to restore or reconstruct normal ocular alignment, obtain normal visual acuity in each eye, to obtain or improve fusion, to eliminate any associated sensory adaptations or diplopia, and to improve visual fields.

Note:  Please see the following document for additional information on strabismus:

Clinical Indications

Medically Necessary:

Adults
Surgical strabismus correction for individuals 18 years of age or older is considered medically necessary for any of the following:

  1. Diplopia; or
  2. Visual confusion; or
  3. Restoration of binocular vision; or
  4. Intolerance of prism glasses or patch; or
  5. Restoration of visual field in individuals with esotropia; or
  6. Elimination or improvement of abnormal head posture; or
  7. Improvement of psychosocial function or vocational status.

Pediatrics
Surgical strabismus correction in individuals less than 18 years of age is considered medically necessary for any of the following:

  1. Infantile esotropia (inward deviation) with onset before 6 months of age; or
  2. Acquired non-accommodative esotropia; or
  3. Partially accommodative esotropia; or
  4. Any deviation due to neural dysfunction, or threatening normal binocular vision; or
  5. Intermittent exotropia (outward deviation); or
  6. Constant exotropia; or
  7. Hyper/hypotropia (vertical deviation); or
  8. Accommodative esotropia that does NOT improve with 3-6 months of refractive correction, patching or when it threatens normal binocular vision.

Not Medically Necessary:

Surgical strabismus correction is considered not medically necessary when the criteria listed above are not met and for all other indications.

Coding

The following codes for treatments and procedures applicable to this guideline are included below for informational purposes. Inclusion or exclusion of a procedure, diagnosis or device code(s) does not constitute or imply member coverage or provider reimbursement policy. Please refer to the member's contract benefits in effect at the time of service to determine coverage or non-coverage of these services as it applies to an individual member.

CPT

 

67311

Strabismus surgery, recession or resection procedure; 1 horizontal muscle

67312

Strabismus surgery, recession or resection procedure; 2 horizontal muscles

67314

Strabismus surgery, recession or resection procedure; 1 vertical muscle (excluding superior oblique)

67316

Strabismus surgery, recession or resection procedure; 2 or more vertical muscles (excluding superior oblique)

67318

Strabismus surgery, any procedure, superior oblique muscle

67320

Transposition procedure (eg, for paretic extraocular muscle), any extraocular muscle

67331

Strabismus surgery on patient with previous eye surgery or injury that did not involve the extraocular muscles

67332

Strabismus surgery on patient with scarring of extraocular muscles (eg, prior ocular injury, strabismus or retinal detachment surgery) or restrictive myopathy (eg, dysthyroid ophthalmopathy)

67334

Strabismus surgery by posterior fixation suture technique, with or without muscle recession

67335

Placement of adjustable suture(s) during strabismus surgery, including postoperative adjustment(s) of suture(s)

67340

Strabismus surgery involving exploration and/or repair of detached extraocular muscle(s)

 

 

ICD-10 Procedure

 

08BL0ZZ

Excision of right extraocular muscle, open approach

08BL3ZZ

Excision of right extraocular muscle, percutaneous approach

08BM0ZZ

Excision of left extraocular muscle, open approach

08BM3ZZ

Excision of left extraocular muscle, percutaneous approach

08QL0ZZ

Repair right extraocular muscle, open approach

08QL3ZZ

Repair right extraocular muscle, percutaneous approach

08QM0ZZ

Repair left extraocular muscle, open approach

08QM3ZZ

Repair left extraocular muscle, percutaneous approach

08SL0ZZ

Reposition right extraocular muscle, open approach

08SL3ZZ

Reposition right extraocular muscle, percutaneous approach

08SM0ZZ

Reposition left extraocular muscle, open approach

08SM3ZZ

Reposition left extraocular muscle, percutaneous approach

 

 

ICD-10 Diagnosis

 

 

All diagnoses

Discussion/General Information

Strabismus refers to the misalignment of the eyes which may result in impaired binocular vision and depth perception, amblyopia, diplopia, visual confusion, or suppression of vision of one eye.  The brain may learn to ignore the input from one eye, causing permanent vision loss in that eye (one type of amblyopia) (AAO, 2012).  Surgical strabismus correction is performed to restore or reconstruct normal ocular alignment, obtain normal visual acuity in each eye, to obtain or improve fusion, to eliminate any associated sensory adaptations or diplopia, and to improve visual fields.

Adults

In 2012, the American Association for Pediatric Ophthalmology and Strabismus (AAPOS) and the American Academy of Ophthalmology (AAO) updated the Adult Strabismus Surgery joint policy statement.  The indications for surgical intervention for adults with strabismus to restore and reconstruct normal ocular alignment include:

Visual and psychological disabilities may result from adult strabismus.  The 2012 policy statement on adult strabismus by the AAPOS/AAO noted adult strabismus may be related to a “Medical or neurological condition such as diabetes, thyroid/Graves' disease, myasthenia gravis, brain tumor, head trauma, or stroke.”  In addition, an individual with childhood strabismus may develop diplopia as an adult.  In the past, many eye doctors thought the treatment of misaligned eyes in adults could not be treated successfully.  Even today, affected individuals may not be offered appropriate surgical treatment because of the misconception that adult strabismus cannot be treated.

Successful strabismus surgery can “Relieve diplopia and visual confusion, restore or reestablish depth perception, expand the visual field, eliminate an abnormal head posture and improve psychological function” (AAPOS/AAO, 2012).  Advances in the management of misaligned eyes may provide benefits to most adults as well as children.

Liebermann and colleagues (2014) reported improvement in health-related quality of life (HRQOL) using the Adult Strabismus 20 (AS-20) questionnaire.  This retrospective review focused on nondiplopic adults that had childhood onset strabismus and had corrective surgery with pre- and post-AS-20 results available.  Statistically significant improvement (p<0.05) in 9 out of 10 function-related questions were noted.  The authors noted these results suggest function-related benefits for adults who had surgical strabismus surgery.  However, the limitations of the study include the small number of participants (n=20) who met inclusion criteria, and the retrospective approach.  The authors noted ongoing study of HRQOL in adults with surgical correction for strabismus is needed to verify their results.

Pediatrics

The development of binocularity is the goal in children, especially the very young.  Evidence suggests that early alignment of the eyes in young children may improve the prognosis for binocular vision.  The American Optometric Association (AOA, 2012) reported for children with infantile esotropia, “Achieving binocular alignment early in life (before age 2 years) to within 10 prism diopters of orthotropia increases the likelihood of achieving binocularity.”  The AAO (2012) notes acquired esotropia occurs more frequently than infantile esotropia, and those with “Early onset acquired esotropia are more likely to require extraocular muscle surgery despite correction of their refractive error with eyeglasses.”  Prompt surgical realignment in individuals with decompensated accommodative esotropia appears to improve the quality of stereopsis.  Early surgery is indicated for those with constant infantile-onset exotropia to improve sensory outcomes.

The AOA notes in the preferred practice pattern guideline Esotropia and Exotropia (2012) there are multiple factors involved in the timing and urgency for surgical referral, including but not limited to the type of strabismus; age of the child; and the likelihood of improving fusion.  Children with infantile strabismus requiring surgical correction should ideally undergo surgery prior to 2 years of age.  Development of binocularity with limited stereopsis have been demonstrated in studies when surgery is performed at an early age and when the duration of ocular misalignment has not been extensive.

There are multiple modalities utilized to address esotropia and exotropia, which may include (AAO, 2012):

Eleven studies satisfied the eligibility criteria of a systematic review of the treatment of childhood intermittent exotropia, X(T).  Seven studies compared unilateral to bilateral resection. Four studies compared surgical to non-surgical interventions.  While surgical interventions appeared to be more effective than non-surgical interventions in improving the angle of deviation, the authors note that the studies were of limited extent and quality with hetergenous outcomes assessments and timeframes (Joyce, 2015).

In general, recovery from strabismus surgery is rapid, and serious complications are uncommon.  Common postoperative effects include nausea and vomiting which can be treated with antiemetics.  Discomfort (scratchy sensation) is usually mild after the procedure.  During the first 24 to 48 hours, a small amount of blood-tinged discharge from the operated eye(s) is a normal occurrence.  It may take several weeks to months for the redness to disappear.  Temporary double vision may occur after surgery, more commonly in adults and children older than 6 years of age.  Postoperative infection is an infrequent complication (AAPOS, 2012; National Institutes of Health, 2012).

Definitions

Amblyopia: Vision in one of the eyes is reduced because the eye and the brain are not working together properly.  The eye itself looks normal, but it is not being used normally because the brain is favoring the other eye.  This condition is also sometimes called lazy eye.

Binocular: Referring to the use of both eyes.

Hypotropia: A classification of strabismus with the eyes turning in a downward direction.

Orthotropia: The absence of strabismus.

Prism diopter: The customary unit of measurement of the magnitude of deviation of the visual axes in strabismus.  One prism diopter is the angle subtended by a deviation of 1 centimeter at a distance of 1 meter.

References

Peer Reviewed Publications:

  1. Alam D, Khan AA, Bani SA, et al. Gain beyond cosmesis: demonstration of psychosocial and functional gains following successful strabismus surgery using the adult strabismus questionnaire adult strabismus 20. Indian J Ophthalmol. 2014; 62(7):799-803.
  2. Beauchamp GR1, Black BC, Coats DK, et al. The management of strabismus in adults--II. Patient and provider perspectives on the severity of adult strabismus and on outcome contributors. J AAPOS. 2005; 9(2):141-147.
  3. Beauchamp GR1, Felius J, Stager DR, Beauchamp CL. The utility of strabismus in adults. Trans Am Ophthalmol Soc. 2005; 103:164-171; discussion 171-172.
  4. Bradbury JA, Taylor RH. Severe complications of strabismus surgery. J AAPOS. 2013; 17(1):59-63.
  5. Gusek-Schneider G, Boss A. Results following eye muscle surgery for secondary sensory strabismus. Strabismus. 2010; 18(1):24-31.
  6. Joyce KE, Beyer F, Thomson RG, Clarke MP. A systematic review of the effectiveness of treatments in altering the natural history of intermittent exotropia. Br J Ophthalmol. 2015; 99(4):440-450.
  7. Kushner BJ. The benefits, risks, and efficacy of strabismus surgery in adults. Optom Vis Sci. 2014; 91(5):e102-109.
  8. Liebermann L, Hatt SR, Leske DA, Holmes JM. Improvement in specific function-related quality-of-life concerns after strabismus surgery in nondiplopic adults. J AAPOS. 2014; 18(2):105-119.
  9. McBain HB1, Au CK2, Hancox J3, et al. The impact of strabismus on quality of life in adults with and without diplopia: a systematic review. Surv Ophthalmol. 2014; 59(2):185-191.
  10. Mets MB1, Beauchamp C, Haldi BA. Binocularity following surgical correction of strabismus in adults. J AAPOS. 2004; 8(5):435-438.
  11. Mills MD, Coats DK, Donahue SP, et al. Strabismus surgery for adults: a report by the American Academy of Ophthalmology. Ophthalmology. 2004; 111(6):1255-1262.
  12. Pineles SL, Demer JL, Isenberg SJ, Birch EE, Velez FG. Improvement in binocular summation after strabismus surgery. JAMA Ophthalmol. 2015; 133(3):326-332.
  13. Ribeiro Gde B, Bach AG, Faria CM, et al. Quality of life of patients with strabismus. Arq Bras Oftalmol. 2014; 77(2):110-113.

Government Agency, Medical Society, and Other Authoritative Publications:

  1. American Academy of Ophthalmology Pediatric Ophthalmology/Strabismus Panel. Preferred Practice Pattern® Guidelines. Amblyopia. San Francisco, CA: American Academy of Ophthalmology; 2012. For additional information visit the AAO website: http://one.aao.org/ppp. Accessed on February 15, 2018.
  2. American Association for Pediatric Ophthalmology and Strabismus and the American Academy of Ophthalmology. Adult strabismus surgery joint policy statement. 2013. For additional information visit the AAO website: http://one.aao.org/ppp. Accessed on February 15, 2018.
  3. American Academy of Ophthalmology Pediatric Ophthalmology/Strabismus Panel. Preferred Practice Pattern® Guidelines. Esotropia and Exotropia. San Francisco, CA: American Academy of Ophthalmology; 2012. For additional information visit the AAO website: https://www.aao.org/guidelines-browse?filter=preferredpracticepatterns. Accessed on February 15, 2018.
  4. American Optometric Association. Optometric clinical practice guideline. Care of the patient with strabismus: esotropia and exotropia. CPG-12. Revised 2010. Available at: https://www.aoa.org/documents/optometrists/CPG-12.pdf. Accessed on February 15, 2018.
  5. Centers for Disease Control and Prevention. Vision Health Initiative. April 23, 2013. Available at: https://www.cdc.gov/visionhealth/basics/index.html. Accessed on February 15, 2018.
  6. Elliott S, Shafiq A. Interventions for infantile esotropia. Cochrane Database Syst Rev. 2013; (7):CD004917.
  7. Hatt SR, Gnanaraj L. Interventions for intermittent exotropia. Cochrane Database Syst Rev. 2013; (5):CD003737.
  8. Korah S, Philip S, Jasper S, et al. Strabismus surgery before versus after completion of amblyopia therapy in children. Cochrane Database Syst Rev. 2014; (10):CD009272.
Websites for Additional Information
  1. American Association for Pediatric Ophthalmology and Strabismus. Available at: http://www.aapos.org/. Accessed on February 15, 2018.
    • Strabismus. Updated February 12, 2018.
    • Adult Strabismus. Updated November 2016.
  2. National Eye Institute (NEI). Amblyopia. Available at: https://nei.nih.gov/health/amblyopia. Accessed on February 15, 2018.
  3. National Institutes of Health. MedlinePlus. Strabismus and related topics. Available at: https://www.nih.gov/. Accessed on February 15, 2018.
  4. Stephenson M. How to take on strabismus in adults. Review of Ophthalmology. October 5, 2015. Available at: https://www.reviewofophthalmology.com/article/how-to-take-on-strabismus-in-adults. Accessed on February 15, 2018.
Index

Strabismus

The use of specific product names is illustrative only. It is not intended to be a recommendation of one product over another, and is not intended to represent a complete listing of all products available.

History

Status

Date

Action

Reviewed

02/27/2018

Medical Policy & Technology Assessment Committee (MPTAC) review. The document header wording was updated from “Current Effective Date” to “Publish Date.” Updated References section.

Reviewed

02/02/2017

MPTAC review. Updated formatting in Clinical Indications section. Updated References and Websites sections.

Reviewed

02/04/2016

MPTAC review. Updated Discussion, References and Websites sections.

Revised

02/05/2015

MPTAC review. Clarified Clinical Indications. Updated Description, Discussion and References sections.

New

02/13/2014

MPTAC review. Initial document development.